Background Associated neurospinal dysraphism in combination with anomalies of the genitourinary tract is well known in children with imperforate anus. There is a broad spectrum of concomittant anomalies with the OEIS Syndrome as the most serious endpoint. OEIS is an acronym for omphalocele, exstrophy (bladder exstrophy/cloacal exstrophy), imperforate anus and spinal defects. At present almost all cases of OEIS are diagnosed prenatally and the patients should be treated at a specialized center with a multidisciplinary team. The complex diagnostic procedures and surgical measures are addressed as well as the difficulties in achieving continence in these patients. Materials and methods We present data of six patients with imperforate anus and spinal dysraphism (4 with meningomyelocele, two with lipomeningocele) currently managed in the spina bifida clinic of the Children’s Hospital of Cologne. Two of them presenting the complete OEIS syndrome symptoms, another two with cloacal exstrophy without omphalocele and two with major renal malformations. Only two of six patients had hydrocephalus. Results

Cora Städtler

Reinhold Cremer

Spinal dysraphism associated with OEIS complex: aspects of diagnosis and treatment

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