Marfan syndrome is a connective tissue disease with typical clinical signs and cardiac involvement. Its appearance in the neonatal period has a bad prognosis due to incompetence of all cardiac valves with subsequent congestive heart failure. Conservative management usually fails, the children die during their first year of life. We report on a girl with neonatal Marfan syndrome who suffered from regurgitance of all cardiac valves, enlarged ventricles, and dilated great arteries. She was NYHA class IV. At the age of six months she underwent heart transplantation. To prevent aneurysm formation and dissection of the great vessels, the whole aortic arch and pulmonary trunk were replaced as well.

T. Krasemann

S. Kotthoff

H.-G. Kehl

V. Debus

T. D. T. Tjan

C. Schmid

J. Vogt

H. H. Scheld

The thoracic and cardiovascular surgeon. Supplement

Thoracic and Cardiovascular Surgeon, Supplement

Cardiac Transplantation in Neonatal Marfan Syndrome - A Life-Saving Approach

新生儿马凡综合征的心脏移植 - 一种救命的方法

Cardiac Transplantation in Neonatal Marfan Syndrome - A Life-Saving Approach

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