Auditory Neuropathy Spectrum Disorders (ANSD) are new classification which was proposed in 2008 by Colorado Children’s Hospital Group and defined as normal otoacoustic emissions and absent ABRs in newborn. In our long term follow up study, hearing of ANSD are changed into three types. Type I is normal OAE and normal ABR (normal hearing), Type II is absent OAE and absent ABR (profound sensoryneural hearing loss), Type III is normal OAE and absent ABR (true auditory neuropathy). However, still complications of vestibular problems in ANSD are not known so far. Historically, in the same year of 1996, a new type of bilateral hearing disorder was reported by Kaga et al. and Starr et al. in different journals. Auditory nerve disease paper was published in the Scandinavian Audiology by Dr. Kaga and Auditory Neuropathy paper was published in Brain. At present, these different terms are considered to be identical in pathophygiology. The auditory nerve disease or auditory neuropathy is a disorder characterized by mild-to-moderate pure-tone hearing loss, poor speech discrimination, absent ABR but normal cochlear outer hair cell function revealed by normal OAE and –SP of Electrocochleography. A variety of processes and etiologies are thought to be involved in the pathophygiology. Most of the reports in the literature discuss auditory profiles and gene mutation of OTOF or OPA1 of patients only but not pathophygiology. Auditory nerve components consist of cochlear nerve, superior vestibular nerve and inferior vestibular nerve. My question is which nerve of these auditory nerve components is involved in AN? We reported our results of auditory and * Corresponding author: Laboratory of Auditory

Auditory neuropathy and auditory neuropathy spectrum disorders

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Journal Info

Category	Quartile
OTORHINOLARYNGOLOGY	4